Dysplasia Epiphysealis Hemimelica of the Carpus

Dysplasia epiphysealis hemimelica (Trevor’s disease) is a rare developmental disorder characterized by unilateral, asymmetrical proliferation of epiphyseal cartilage. Cases involving the upper extremity are unusual. Three cases, the largest series to date, involving dysplasia epiphysealis hemimelica of the carpus, are discussed here. Two of the patients had been treated previously at other institutions where their disorders were not recognized. The purpose of this article is to present a clear description of this disorder and its natural course. A treatment algorithm is also recommended. Needless workup, treatment, and anxiety of the patient and family can be avoided by an early, accurate diagnosis. (Journal of Surgical Orthopaedic Advances 14(1):42–47, 2005)